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Author Notes:

Andrew J Kirsch Emory University, Children’s Healthcare of Atlanta, 5730 Glenridge Drive, Suite 200, Atlanta, GA 30328, USA Tel +1 404 252 5206 Fax +1 404 252 1268 Email: akirschmd@gmail.com

The authors report no conflicts of interest in this work.

Subject:

Keywords:

  • abdominal wall laxity
  • abdominoplasty
  • cryptorchidism
  • prune-belly syndrome
  • urinary tract dilation

Prune belly syndrome: current perspectives.

Tools:

Journal Title:

Pediatric Health, Medicine and Therapeutics

Volume:

Volume 10

Publisher:

, Pages 75-81

Type of Work:

Article | Final Publisher PDF

Abstract:

Prune belly syndrome (PBS) is a rare but morbid congenital disease, classically defined by a triad of cardinal features that includes cryptorchidism, urinary tract dilation and laxity of the abdominal wall musculature. Children often require numerous surgical interventions including bilateral orchidopexy as well as individually tailored urinary tract and abdominal wall reconstruction. Along with the classic features, patients with PBS often experience gastrointestinal, orthopedic, and cardiopulmonary comorbidities.

Copyright information:

Copyright © 2019 Arlen et al.

This is an Open Access work distributed under the terms of the Creative Commons Attribution-Noncommercial 3.0 Unported License (https://creativecommons.org/licenses/by-nc/3.0/).
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